{"id":932,"date":"2013-10-13T11:13:50","date_gmt":"2013-10-13T09:13:50","guid":{"rendered":"http:\/\/slanedeti.sk\/cms\/ine-ochorenia-a-dosledky-cf-2\/201310"},"modified":"2013-12-31T17:33:31","modified_gmt":"2013-12-31T16:33:31","slug":"ine-ochorenia-a-dosledky-cf-2","status":"publish","type":"post","link":"https:\/\/slanedeti.sk\/cms\/ine-ochorenia-a-dosledky-cf-2\/932","title":{"rendered":"In\u00e9 ochorenia a d\u00f4sledky CF"},"content":{"rendered":"<p>Cystick\u00fa fibr\u00f3zu komplikuje a modifikuje mno\u017estvo \u010fal\u0161\u00edch mimop\u013e\u00facnych a mimotr\u00e1viacich probl\u00e9mov. K t\u00fdm naj\u010dastej\u0161ie sa vyskytuj\u00facim patria: porucha potn\u00fdch \u017eliaz, plodnos\u0165, postihnutie k\u013abov.<\/p>\n<p><strong>Porucha potn\u00fdch \u017eliaz<\/strong>, pri ktorej vo v\u00fdvodoch potn\u00fdch \u017eliaz nedoch\u00e1dza k sp\u00e4tnej resorbcii chloridu a sod\u00edka, preto je v pote vysok\u00e1 koncentr\u00e1cia soli. Potn\u00fd test je z\u00e1kladn\u00fdm diagnostick\u00fdm vy\u0161etren\u00edm pri cystickej fibr\u00f3ze.<\/p>\n<p><strong>Fertilita (plodnos\u0165)<\/strong> &#8211; u pacientov s CF doch\u00e1dza tie\u017e k poruch\u00e1m reproduk\u010dn\u00fdch org\u00e1nov. Sterilita je \u010dastej\u0161ia u mu\u017eov a d\u00f4vodom b\u00fdva porucha transportu spermii a atrofia \u0161trukt\u00far semenovodu. U \u017eien to m\u00f4\u017ee by\u0165 najm\u00e4 tvorba v\u00e4zk\u00e9ho hlienu v delo\u017enom hrdle. Pri gravidite sa za rizikov\u00e9 pova\u017euj\u00fa pacientky s CF s hodnotami FEV &lt; 50%, BMI &lt; 18, s cukrovkou a chronickou koloniz\u00e1ciou Burkhold\u00e9ria cep\u00e1cia. Nie je neobvykl\u00e9, \u017ee pacienti s CF maj\u00fa zdrav\u00e9 deti.<\/p>\n<p><strong>Osteopor\u00f3za<\/strong> \u2013 rednutie kost\u00ed sa ve\u013emi \u010dasto vyv\u00edja u dospel\u00fdch pacientov s CF a sp\u00f4sobuje ju zl\u00fd stav v\u00fd\u017eivy, pr\u00edtomnos\u0165 CFTR v skelet\u00e1rnom syst\u00e9me, zv\u00fd\u0161en\u00e1 tvorba TNF alfa, ktor\u00fd p\u00f4sob\u00ed ako potentn\u00fd inhib\u00edtor kostn\u00e9ho kolag\u00e9nu, zn\u00ed\u017een\u00e1 fyzick\u00e1 aktivita a zna\u010dn\u00fdm rizikom je lie\u010dba syst\u00e9mov\u00fdmi kortikosteroidmi. Predstup\u0148om osteopor\u00f3zy je osteop\u00e9nia, ktor\u00e1 sa e\u0161te nemus\u00ed lie\u010di\u0165 ako osteopor\u00f3za, ale pova\u017euje sa za rizikov\u00fd faktor jej vzniku. Pre potencion\u00e1lnu hrozbu tohto ochorenia u pacientov s CF, patr\u00ed k \u0161tandartnej starostlivosti monitorovanie kostnej denzity, sledovanie hladiny vitam\u00ednu D v krvi a snaha o normaliz\u00e1ciu cel\u00e9ho nutri\u010dn\u00e9ho stavu pacienta. Pri lie\u010dbe sa pod\u00e1va vit. D, vit. K, bisfosfon\u00e1ty, kalciton\u00edn<\/p>\n<div style=\"text-align: center;\"><img loading=\"lazy\" decoding=\"async\" class=\"aligncenter\" style=\"border: 0px; margin-top: 20px; margin-bottom: 20px;\" title=\"osteoporoza\" alt=\"osteoporoza\" src=\"https:\/\/slanedeti.sk\/cms\/picture_migration\/osteoporoza.jpg\" width=\"450\" height=\"600\" border=\"0\" \/><\/div>\n<p><strong>Postihnutie k\u013abov s reumatick\u00fdmi sympt\u00f3mami<\/strong> s\u00fa pri CF relat\u00edvne \u010dast\u00e9. K naj\u010dastej\u0161\u00edm postihnutiam k\u013abov u pacientov s CF patr\u00ed hypertrofick\u00e1 pulmon\u00e1rna osteoartropatia &#8211; HPO, pre ktor\u00fa s\u00fa pr\u00edzna\u010dn\u00e9 napr. \u201epali\u010dkovit\u00e9 prsty\u201c (charakteristick\u00e9 pre vonkaj\u0161\u00ed prejav ne\u0161pecifick\u00e9ho chronick\u00e9ho p\u013e\u00facneho ochorenia) a tie\u017e postihnutia dist\u00e1lnych k\u013abov kon\u010dat\u00edn a periodick\u00e1 artrit\u00edda. U pacientov s CF sa \u010dasto objavuje epizodick\u00e1 artrit\u00edda \u2013 z\u00e1palov\u00e9 po\u0161kodenie k\u013abov (boles\u0165, opuch, za\u010dervenanie) a m\u00f4\u017ee ma\u0165 ak\u00fatnu alebo subak\u00fatnu formu. Diagn\u00f3za sa stanovuje na z\u00e1klade klinick\u00fdch prejavov, r\u00f6ntgenov\u00fdm vy\u0161etren\u00edm, ako aj laborat\u00f3rnym vy\u0161etren\u00edm reumatoidn\u00fdch faktorov v krvi. Liekmi prvej vo\u013eby s\u00fa nesteroidov\u00e9 protiz\u00e1palov\u00e9 lieky (tzv. antiflogistik\u00e1). \u010ealej s\u00fa to glukokortikoidy, lieky modifikuj\u00face chorobu (metotrex\u00e1t, penicilam\u00edn&#8230;), fyzioterapia a rehabilit\u00e1cia.<\/p>\n<p>&nbsp;<\/p>\n<h4><strong>Psychologick\u00e9 a psychosoci\u00e1lne d\u00f4sledky CF<\/strong><\/h4>\n<p>Cystick\u00e1 fibr\u00f3za je obmedzuj\u00face ochorenie, ktor\u00e9 radik\u00e1lne men\u00ed be\u017en\u00fd denn\u00fd re\u017eim pacienta. Mus\u00ed sa do\u0148 implementova\u0165 nieko\u013ekohodinov\u00e9 inhalovanie, dychov\u00e1 rehabilit\u00e1cia, kondi\u010dn\u00e9 cvi\u010denia, pravideln\u00e1 medik\u00e1cia, vysokoenergetick\u00e1 strava s pr\u00edjmom niektor\u00fdch \u0161pecifick\u00fdch zlo\u017eiek stravy. Okrem op\u00edsan\u00fdch lie\u010debn\u00fdch proced\u00far sprev\u00e1dzaj\u00fa pacienta aj samotn\u00e9 prejavy ochorenia ako ka\u0161e\u013e, expektor\u00e1cia, potenie, pre zhor\u0161enie zdravotn\u00e9ho stavu opakovan\u00e9 absencie v \u0161kole a v pr\u00e1ci, ktor\u00e9 s\u00fa negat\u00edvne prij\u00edman\u00e9 okol\u00edm, \u010doho d\u00f4sledkom s\u00fa pacienti s CF vystavovan\u00ed v priebehu svojho \u017eivota r\u00f4znym psychosoci\u00e1lnym probl\u00e9mom v rodine, v \u0161kole v zamestnan\u00ed, ale aj v priate\u013esk\u00fdch a partnersk\u00fdch vz\u0165ahoch. Niektor\u00ed s ochoren\u00edm vyrastaj\u00fa od detstva a vtedy naj\u0165a\u017e\u0161ie bremeno spo\u010d\u00edva na rodi\u010doch, ktor\u00ed sa \u010dasto vzd\u00e1vaj\u00fa svojej kari\u00e9ry a plne sa venuj\u00fa chor\u00e9mu die\u0165a\u0165u. V s\u00fa\u010dasnosti nie je ni\u010d v\u00fdnimo\u010dn\u00e9, \u017ee cystick\u00e1 fibr\u00f3za sa diagnostikuje aj v dospelom veku a vtedy sa pacient pasuje so spracovan\u00edm reality ove\u013ea \u0165a\u017e\u0161ie. Ka\u017ed\u00fd pacient a ka\u017ed\u00fd vek si vy\u017eaduje in\u00fd individu\u00e1lny pr\u00edstup, pri ktorom je \u010dasto potrebn\u00e1 intervencia psychol\u00f3gov, psychiatrov a soci\u00e1lnych pracovn\u00edkov, ktor\u00ed patria do \u0161tandardn\u00e9ho CF t\u00edmu v r\u00e1mci komplexnej starostlivosti. \u00da\u010dinn\u00e1 lie\u010dba a zv\u00fd\u0161en\u00e1 zdravotn\u00e1 starostlivos\u0165 zvy\u0161uje pacientom s CF kvalitu \u017eivota. V\u00fdznamne ju m\u00f4\u017ee ovplyvni\u0165 a zv\u00fd\u0161i\u0165 porozumenie v rodine, pochopenie najbli\u017e\u0161ieho okolia a pomoc povolan\u00fdch pri rie\u0161en\u00ed ich legit\u00edmnych soci\u00e1lnych probl\u00e9mov. Iba v kontexte v\u0161etk\u00fdch t\u00fdchto faktorov m\u00f4\u017eu pacienti s CF \u017ei\u0165 \u017eivot be\u017en\u00fdch \u013eud\u00ed.<\/p>\n<p><em>Zdroj: \u010derpan\u00e9 z odbornej pr\u00e1ce MUDr. Branislava Remi\u0161a<br \/>\nKlinika pneumol\u00f3gie a ftizeol\u00f3gie I. SZU, Univerzitn\u00e1 nemocnica Bratislava<br \/>\n<\/em><strong><\/strong><\/p>\n<h5><\/h5>\n<h4><strong><br \/>\nZ\u00e1vere\u010dn\u00e1 pozn\u00e1mka autorky s\u00e9rie \u010dl\u00e1nkov o cystickej fibr\u00f3ze<\/strong><\/h4>\n<p><strong><\/strong><em>Cystick\u00e1 fibr\u00f3za m\u00e1 oporu aj v pr\u00e1vnom syst\u00e9me. Odborn\u00e9 usmernenie MZ SR o poskytovan\u00ed zdravotnej starostlivosti pacientom s cystickou fibr\u00f3zou \u010d. Z55242\/2010 \u2013 OZS upravuje komplexn\u00fa zdravotn\u00fa starostlivos\u0165 o pacienta s CF v Centr\u00e1ch CF, ich materi\u00e1lno technick\u00e9 vybavenie, hygienick\u00fd re\u017eim, diagnostick\u00fd a lie\u010debn\u00fd postup \u0161pecializovanej zdravotnej starostlivosti v Centr\u00e1ch CF.<\/em><\/p>\n<p><em>Podporu soci\u00e1lneho za\u010dlenenia osoby s \u0165a\u017ek\u00fdm zdravotn\u00fdm postihnut\u00edm do spolo\u010dnosti rie\u0161i z\u00e1k. \u010d.447\/2008 Z.z. o pe\u0148a\u017en\u00fdch pr\u00edspevkoch na kompenz\u00e1ciu \u0165a\u017ek\u00e9ho zdravotn\u00e9ho postihnutia. Pacienti s CF pri uplat\u0148ovan\u00ed si n\u00e1rokov z uveden\u00e9ho z\u00e1kona maj\u00fa najv\u00e4\u010d\u0161\u00ed probl\u00e9m pri prizn\u00e1van\u00ed pe\u0148a\u017en\u00e9ho pr\u00edspevku na osobn\u00e9 motorov\u00e9 vozidlo a \u010dasto pre nepochopenie \u00faradn\u00edkov, ktor\u00ed nemaj\u00fa o cystickej fibr\u00f3ze vedomos\u0165, svoj n\u00e1rok nedosiahnu. Zmiernenie alebo rie\u0161enie nepriaznivej soci\u00e1lnej situ\u00e1cie upravuje z\u00e1k. \u010d. 448\/2008 Z.z. o soci\u00e1lnych slu\u017eb\u00e1ch. Aktu\u00e1lny pre pacientov s cystickou fibr\u00f3zou s\u00fa v tejto pr\u00e1vnej norme ustanovenia o n\u00e1roku na opatrovate\u013esk\u00fd pr\u00edspevok, podmienky ktor\u00e9ho nezoh\u013ead\u0148uj\u00fa cystick\u00fa fibr\u00f3zu \u00faplne objekt\u00edvne.<\/em><br \/>\n<em> Na pomoc pacientom s CF vznikli pacientsk\u00e9 organiz\u00e1cie: Priatelia slan\u00fdch det\u00ed, Klub cystickej fibr\u00f3zy a Slovensk\u00e1 Asoci\u00e1cia Cystickej Fibr\u00f3zy s cie\u013eom poskytova\u0165 soci\u00e1lne poradenstvo, individu\u00e1lnu finan\u010dn\u00fa a materi\u00e1lnu pomoc, rozv\u00edja\u0165 medzin\u00e1rodn\u00e9 aktivity, obhajova\u0165 pr\u00e1va, potreby a z\u00e1ujmy pacientov s CF a informova\u0165 verejnos\u0165 a \u0161\u00edri\u0165 osvetu o tomto ochoren\u00ed. Tie\u017e sa podie\u013eaj\u00fa na tvorbe soci\u00e1lnych z\u00e1konov a sna\u017eia sa svojimi n\u00e1vrhmi upravova\u0165 ustanovenia, ktor\u00e9 komplikuj\u00fa pacientom s CF \u017eivot.<\/em><\/p>\n","protected":false},"excerpt":{"rendered":"<p>Cystick&uacute; fibr&oacute;zu komplikuje a modifikuje mno&#382;stvo &#271;al&scaron;&iacute;ch mimop&#318;&uacute;cnych a mimotr&aacute;viacich probl&eacute;mov. K t&yacute;m naj&#269;astej&scaron;ie sa vyskytuj&uacute;cim patria: porucha potn&yacute;ch &#382;liaz, plodnos&#357;, postihnutie k&#314;bov. Porucha potn&yacute;ch &#382;liaz, pri ktorej vo v&yacute;vodoch potn&yacute;ch &#382;liaz nedoch&aacute;dza k sp&auml;tnej resorbcii chloridu a sod&iacute;ka, preto &hellip; <a href=\"https:\/\/slanedeti.sk\/cms\/ine-ochorenia-a-dosledky-cf-2\/932\">Continued<\/a><\/p>\n","protected":false},"author":6,"featured_media":984,"comment_status":"closed","ping_status":"closed","sticky":false,"template":"","format":"standard","meta":{"kt_blocks_editor_width":"","footnotes":""},"categories":[253],"tags":[],"class_list":["post-932","post","type-post","status-publish","format-standard","has-post-thumbnail","hentry","category-o-cystickej-fibroze"],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v27.5 - https:\/\/yoast.com\/product\/yoast-seo-wordpress\/ -->\n<title>In\u00e9 ochorenia a d\u00f4sledky CF - Slan\u00e9 deti<\/title>\n<meta name=\"description\" content=\"Cystick\u00fa fibr\u00f3zu komplikuje mno\u017estvo \u010fal\u0161\u00edch mimop\u013e\u00facnych a mimotr\u00e1viacich probl\u00e9mov: porucha potn\u00fdch \u017eliaz, plodnos\u0165, postihnutie k\u013abov.\" \/>\n<meta name=\"robots\" content=\"index, follow, max-snippet:-1, max-image-preview:large, max-video-preview:-1\" \/>\n<link rel=\"canonical\" href=\"https:\/\/slanedeti.sk\/cms\/ine-ochorenia-a-dosledky-cf-2\/932\" \/>\n<meta property=\"og:locale\" content=\"sk_SK\" \/>\n<meta property=\"og:type\" content=\"article\" \/>\n<meta property=\"og:title\" content=\"In\u00e9 ochorenia a d\u00f4sledky CF - 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