{"id":913,"date":"2012-10-02T08:22:47","date_gmt":"2012-10-02T06:22:47","guid":{"rendered":"http:\/\/slanedeti.sk\/cms\/cysticka-fibroza-aspergiloza-2\/201210"},"modified":"2014-04-07T16:13:53","modified_gmt":"2014-04-07T15:13:53","slug":"cysticka-fibroza-aspergiloza-2","status":"publish","type":"post","link":"https:\/\/slanedeti.sk\/cms\/cysticka-fibroza-aspergiloza-2\/913","title":{"rendered":"Cystick\u00e1 fibr\u00f3za: Aspergil\u00f3za"},"content":{"rendered":"<p>Aspergil\u00f3za je z\u00e1va\u017en\u00e1 komplik\u00e1cia pri CF, s ktorou sa v poslednom \u010dase stret\u00e1vame \u010doraz \u010dastej\u0161ie. Vyvol\u00e1vaj\u00fa ju vl\u00e1knit\u00e9 huby rodu Aspergillus, ktor\u00e9 s\u00fa v \u017eivotnom prostred\u00ed ve\u013emi roz\u0161\u00edren\u00e9 (napr. v p\u00f4de, zdrav. zariadeniach, vo ventila\u010dn\u00fdch syst\u00e9moch, v kontaminovanom prachu pri rekon\u0161truk\u010dn\u00fdch pr\u00e1cach a v \u010fal\u0161\u00edch in\u00fdch materi\u00e1loch).<\/p>\n<p>Do d\u00fdchac\u00edch ciest sa dost\u00e1vaj\u00fa vd\u00fdchnut\u00edm sp\u00f3r a v predisponovanom prostred\u00ed s hust\u00fdm hlienom sa m\u00f4\u017eu zachyti\u0165 a r\u00e1s\u0165.<\/p>\n<p>Pod\u013ea patogen\u00e9zy a imunitnej odpovede pozn\u00e1me aspergil\u00f3zu:<br \/>\n<em>Saprofytick\u00fa<\/em>,\u00a0ktor\u00e1 je pri CF \u010dast\u00e1. Jednoduch\u00e1 koloniz\u00e1cia d\u00fdchac\u00edch ciest bez klinick\u00fdch prejavov a jedn\u00fdm z faktorov vzniku je dlhodob\u00e1 antibiotick\u00e1 lie\u010dba.<\/p>\n<p><em>Invaz\u00edvnu<\/em>,\u00a0ktor\u00e1 sa prejavuje ako z\u00e1va\u017en\u00e9 de\u0161truuj\u00face ochorenie, postihuj\u00face pacientov s imunodeficitom a pri CF sa vyskytuje v\u00fdnimo\u010dne.<\/p>\n<p><em>Alergick\u00fa\u00a0bronchopulmon\u00e1lnu\u00a0aspergil\u00f3zu\u00a0(ABPA),<\/em> ktor\u00e1 vznik\u00e1 vd\u00fdchnut\u00edm h\u00fab a u predisponovan\u00fdch jedincoch sa tieto kolonizuj\u00fa bez inv\u00e1zie do p\u013e\u00facneho tkaniva a m\u00f4\u017eu vyvola\u0165 hypersenzit\u00edvnu odpove\u010f. V patogen\u00e9ze ABPA maj\u00fa v\u00fdznamn\u00fa<br \/>\n\u00falohu aspergily pr\u00edtomn\u00e9 na povrchu respira\u010dn\u00e9ho epitelu, kde rast\u00fa a nesk\u00f4r epitel po\u0161kodzuj\u00fa, a t\u00fdm sa dost\u00e1vaj\u00fa hlb\u0161ie k bronchoalveol\u00e1rnemu lymfoidn\u00e9mu tkanivu. V\u010dasn\u00e1 f\u00e1za hypersenzit\u00edvnej odpovede organizmu zodpoved\u00e1 za bronchospazmus a neskor\u00e1 za de\u0161truk\u010dn\u00e9 zmeny priedu\u0161iek a p\u013e\u00fac.<\/p>\n<div style=\"text-align: center;\"><img loading=\"lazy\" decoding=\"async\" style=\"margin-top: 20px; margin-bottom: 20px; border: 0px;\" title=\"Aspergil\u00f3za\" alt=\"Aspergil\u00f3za\" src=\"https:\/\/slanedeti.sk\/cms\/picture_migration\/201210020822_aspergiloza.jpg\" width=\"400\" height=\"301\" border=\"0\" \/><\/div>\n<h4><strong>Diagnostika<\/strong><\/h4>\n<p>Diagnostika ABPA je zlo\u017eit\u00e1 a preto boli prijat\u00e9 v\u0161eobecn\u00e9 diagnostick\u00e9 krit\u00e9ria:<\/p>\n<ul>\n<li>prejavy bronchi\u00e1lnej astmy<\/li>\n<li>v\u010dasn\u00e1 ko\u017en\u00e1 precitlivenos\u0165 na antig\u00e9n Aspergillus fumigatus<\/li>\n<li>perif\u00e9rna krvn\u00e1 eozinof\u00edlia (&gt;1,0&#215;109 \/L)<\/li>\n<li>migruj\u00face p\u013e\u00facne infiltr\u00e1ty<\/li>\n<li>proxim\u00e1lne bronchiekt\u00e1zie<\/li>\n<li>zv\u00fd\u0161en\u00e1 hladina celkov\u00e9ho s\u00e9rov\u00e9ho IgE (&gt; 1000 ng\/mL)<\/li>\n<li>zv\u00fd\u0161en\u00e9 \u0161pecifick\u00e9 protil\u00e1tky proti A. fumigatus triedy IgE a IgG<\/li>\n<\/ul>\n<p>Hladina celkov\u00e9ho s\u00e9rov\u00e9ho IgE u pacientov s ABPA sa uk\u00e1zala ako ve\u013emi v\u00fdznamn\u00e1 a z\u00e1visl\u00e1 na aktivite ochorenia. Preto je pova\u017eovan\u00e1 za v\u00fdznamn\u00fd marker klinick\u00e9ho mana\u017ementu.<\/p>\n<p>Niekedy sa uv\u00e1dzaj\u00fa aj \u0161t\u00e1dia ABPA za \u00fa\u010delom presnej\u0161ej klasifik\u00e1cie pacientov:<\/p>\n<ol>\n<li>\u0161t\u00e1dium je prv\u00e1 ak\u00fatna f\u00e1za, zv\u00e4\u010d\u0161a so symptomatol\u00f3giou a typick\u00fdmi diagnostick\u00fdmi znakmi.<\/li>\n<li>\u0161t\u00e1dium je remisia, ktor\u00fa m\u00f4\u017eeme dosiahn\u00fa\u0165 lie\u010dbou.<\/li>\n<li>\u0161t\u00e1dium je exacerb\u00e1cia so znakmi podobn\u00fdmi ako pri prvej ak\u00fatnej f\u00e1zy.<\/li>\n<li>\u0161t\u00e1dium je stav kedy doch\u00e1dza k v\u010dasn\u00fdm exacerb\u00e1ciam po ukon\u010den\u00ed lie\u010dby a ozna\u010duje sa ako kortikodependentn\u00e1 ABPA.<\/li>\n<li>\u0161t\u00e1dium je ozna\u010dovan\u00e9 ako \u201eend stage ABPA\u201c a je charakterizovan\u00e9 respira\u010dnou\u00a0insuficienciou, p\u013e\u00facnou fibr\u00f3zou a p\u013e\u00facnou hypertenziou.<\/li>\n<\/ol>\n<h4><strong>Lie\u010dba<\/strong><\/h4>\n<p><strong>Kombin\u00e1cia\u00a0kortikosteroidov\u00a0a\u00a0antimykotickej\u00a0lie\u010dby<\/strong> intraconazolom (Sporanox). Kortikoidy potl\u00e1\u010daj\u00fa hypersenzit\u00edvny z\u00e1pal a cie\u013eom antimykotickej lie\u010dby je zn\u00ed\u017ei\u0165 potrebu kortikosteroidov, zn\u00ed\u017ei\u0165 antig\u00e9nov\u00fa n\u00e1lo\u017e v d\u00fdchac\u00edch cest\u00e1ch, ako aj prevent\u00edvne zamedzi\u0165 vzniku invaz\u00edvnej formy pri lie\u010dbe kortikoidmi. Lie\u010dbou sa zni\u017euje po\u010det kol\u00f3nii v sp\u00fate pacientov s pozitivitou A. fumigatus, zvy\u0161uj\u00fa sa funk\u010dn\u00e9 parametre (FEV1) a zni\u017euje sa hladina celkov\u00e9ho IgE. ABPA m\u00e1 tendenciu k exacerb\u00e1ciam, \u010do si vy\u017eaduje dlhodob\u00fa lie\u010dbu kortikosteroidmi v ni\u017e\u0161\u00edch d\u00e1vkach, alebo opakovan\u00e9 lie\u010dby exacerb\u00e1ci\u00ed vysok\u00fdmi d\u00e1vkami.<br \/>\n<strong>Anti\u00a0IgE\u00a0lie\u010dba<\/strong>\u00a0hum\u00e1nnymi monoklon\u00e1lnymi protil\u00e1tkami proti IgE sa \u010doraz \u010dastej\u0161ie pod\u00e1va pacientom pri opakovan\u00fdch exacerb\u00e1ciach ABPA a tie\u017e ako alternat\u00edvna lie\u010dba t\u00fdm pacientom, ktor\u00ed trpia z\u00e1va\u017en\u00fdmi ne\u017eiad\u00facimi \u00fa\u010dinkami kortikosterteroidnej lie\u010dby.<\/p>\n<p><strong>Inhala\u010dn\u00e9\u00a0kortikoidy<\/strong>\u00a0v r\u00e1mci dlhodobej lie\u010dby pri ABPA prin\u00e1\u0161aj\u00fa uspokojiv\u00e9<br \/>\nv\u00fdsledky. Vzh\u013eadom k riziku vzniku recid\u00edvy ochorenia aj po prelie\u010den\u00ed, je nevyhnutn\u00e9 pacienta sledova\u0165, predch\u00e1dza\u0165 recid\u00edve a t\u00fdm aj dlhodobej lie\u010dbe kortikoidmi a antimykotikami, vzh\u013eadom na ich mo\u017en\u00e9 ved\u013eaj\u0161ie \u00fa\u010dinky.<\/p>\n<p><em>\u010derpan\u00e9 z odbornej pr\u00e1ce MUDr. Branislava Remi\u0161a<br \/>\nKlinika pneumol\u00f3gie a ftizeol\u00f3gie I. SZU, Univerzitn\u00e1 nemocnica Bratislava<\/em><\/p>\n","protected":false},"excerpt":{"rendered":"<p>Aspergil&oacute;za je z&aacute;va&#382;n&aacute; komplik&aacute;cia pri CF, s ktorou sa v poslednom &#269;ase stret&aacute;vame &#269;oraz &#269;astej&scaron;ie. Vyvol&aacute;vaj&uacute; ju vl&aacute;knit&eacute; huby rodu Aspergillus, ktor&eacute; s&uacute; v &#382;ivotnom prostred&iacute; ve&#318;mi roz&scaron;&iacute;ren&eacute; (napr. v p&ocirc;de, zdrav. zariadeniach, vo ventila&#269;n&yacute;ch syst&eacute;moch, v kontaminovanom prachu pri &hellip; <a href=\"https:\/\/slanedeti.sk\/cms\/cysticka-fibroza-aspergiloza-2\/913\">Continued<\/a><\/p>\n","protected":false},"author":6,"featured_media":1122,"comment_status":"closed","ping_status":"closed","sticky":false,"template":"","format":"standard","meta":{"kt_blocks_editor_width":"","footnotes":""},"categories":[253],"tags":[227],"class_list":["post-913","post","type-post","status-publish","format-standard","has-post-thumbnail","hentry","category-o-cystickej-fibroze","tag-aspergiloza"],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v27.5 - https:\/\/yoast.com\/product\/yoast-seo-wordpress\/ -->\n<title>Cystick\u00e1 fibr\u00f3za: Aspergil\u00f3za - Slan\u00e9 deti<\/title>\n<meta name=\"description\" content=\"Aspergil\u00f3za je z\u00e1va\u017en\u00e1 komplik\u00e1cia pri CF, s ktorou sa v poslednom \u010dase stret\u00e1vame \u010doraz \u010dastej\u0161ie.\" \/>\n<meta name=\"robots\" content=\"index, follow, max-snippet:-1, max-image-preview:large, max-video-preview:-1\" \/>\n<link rel=\"canonical\" href=\"https:\/\/slanedeti.sk\/cms\/cysticka-fibroza-aspergiloza-2\/913\" \/>\n<meta property=\"og:locale\" content=\"sk_SK\" \/>\n<meta property=\"og:type\" content=\"article\" \/>\n<meta property=\"og:title\" content=\"Cystick\u00e1 fibr\u00f3za: Aspergil\u00f3za - 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